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血液系統疾病
特發性血小板減少性紫癜

        特(te)發(fa)性血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)減(jian)(jian)少(shao)(shao)(shao)性紫癜(Idiopathic thrombocytopenic purpura,ITP)是(shi)一種由于免疫異常導(dao)致(zhi)血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)自(zi)身抗(kang)體增多(duo), 使得血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)尚(shang)未(wei)成(cheng)熟即被(bei)脾臟(zang)內(nei)皮系統吞噬(shi),從而導(dao)致(zhi)血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)減(jian)(jian)少(shao)(shao)(shao)的一種疾病(bing)。以廣泛皮膚、粘膜或內(nei)臟(zang)出(chu)血(xue)(xue),血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)減(jian)(jian)少(shao)(shao)(shao),骨(gu)髓巨核細胞發(fa)育、成(cheng)熟障礙,血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)生存時間(jian)縮短(duan)及抗(kang)血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)自(zi)身抗(kang)體出(chu)現為(wei)(wei)(wei)特(te)征。ITP可(ke)發(fa)生于各年齡組,兒童ITP發(fa)病(bing)率(lv)略高(gao)于成(cheng)人。發(fa)病(bing)高(gao)峰為(wei)(wei)(wei)2~6歲。75%~82%的兒童ITP在6個月內(nei)可(ke)獲緩解,但大(da)齡兒童(青少(shao)(shao)(shao)年)轉為(wei)(wei)(wei)慢性ITP的可(ke)能性較大(da)。其次(ci),兒童ITP多(duo)為(wei)(wei)(wei)急性型,而成(cheng)人ITP多(duo)為(wei)(wei)(wei)慢性型。抗(kang)血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)抗(kang)體檢(jian)測(ce)(ce)是(shi)鑒別免疫性和非(fei)免疫性血(xue)(xue)小(xiao)板(ban)(ban)(ban)(ban)減(jian)(jian)少(shao)(shao)(shao)的檢(jian)測(ce)(ce)方法,是(shi)臨(lin)床ITP診斷中(zhong)重要的實(shi)驗室檢(jian)測(ce)(ce)手(shou)段。


歐蒙提供產品如下:

檢測指標Ig類(lei)型(xing)方法學基質
血小板抗原IgGIIFT血小板,人(O型血)

IIFT:間接(jie)免疫熒光法